الفهرس 
Outcome of Thoracic Primitive Neuroectodermal Tumors in Pediatrics
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Abstract
Background:Primitive neuroectodermal tumors (PNETs) are malignant and aggressive 2small round cells3 neoplasms that arise from the primitive nerve cells of the central nervous system (central PNETs), but at times, they can affect any peripheral nerve (peripheral PNETs) in the neck, chest wall, retroperitoneum, pelvis, and extremities (Khmou et al., 2016). In 1979, Askin et al. described for the first time, 20 cases of children and adolescents affected by PNETs of the thoracopulmonary region.Since then,PNETs developed within the soft tissue of the thoracopulmonary region are referred to as 2Askin{u2019}s tumors3 [AT] (Triarico et al., 2018).In addition to this, Askin{u2019}s tumors occur typically in children and adolescents and they belong to the Ewing{u2019}s sarcoma (EW) family because of their histological, immunohistochemically, cytogenetic, and phenotypic similarities (Parikh M et al., 2011).Because of the rarity of this neoplasm, the approach to Askin{u2019}s tumors is complex and it may require a multidisciplinary management (Devi LP et al., 2015)